Progressive Systemic Sclerosis

Progressive Systemic Sclerosis (PSS), also known as scleroderma, is a chronic autoimmune disorder that primarily affects the skin, but can also impact internal organs like the heart, lungs, kidneys, and digestive tract. Early diagnosis and treatment are crucial in managing the disease effectively, preventing complications, and enhancing quality of life. At Felix Hospital, a leading rheumatology hospital, we provide specialized care for patients dealing with SPS, offering advanced diagnostic tools and personalized treatment plans tailored to each individual.


Contact Felix Hospital today for a thorough evaluation and customized treatment plan. Call us at +91 9667064100 for appointments.

 

Progressive Systemic Sclerosis is a rare autoimmune disease characterized by the excessive production of collagen, leading to the thickening and hardening of connective tissues. This overproduction of collagen affects not only the skin but also internal organs, making SPS a potentially life-threatening condition if left untreated. The disease progresses over time, impacting various body systems, and requires careful monitoring and comprehensive care.

 

Symptoms of Progressive Systemic Sclerosis

Symptoms of progressive systemic sclerosis vary depending on the extent and severity of the condition, but they typically include:

  • Skin Thickening: Hardening and tightening of the skin, especially on the fingers, hands, face, and forearms.

  • Raynaud’s Phenomenon: A condition where the fingers and toes turn white or blue in response to cold or stress.

  • Joint Pain and Stiffness: Pain, swelling, and stiffness in the joints, often affecting mobility.

  • Gastrointestinal Issues: Difficulty swallowing, acid reflux, bloating, or constipation as the digestive system may become affected.

  • Lung Problems: Shortness of breath and a persistent dry cough due to lung involvement.

  • Heart and Kidney Complications: In severe cases, progressive systemic sclerosis may affect the heart and kidneys, leading to life-threatening complications.

 

Diagnosis of Progressive Systemic Sclerosis at Felix Hospital

Diagnosing SPS involves a combination of clinical evaluations, laboratory tests, and imaging studies. At Felix Hospital, we use advanced diagnostic tools to ensure an accurate and timely diagnosis, which is essential for effective management.

  • Physical Examination: A detailed physical exam to check for skin thickening, joint mobility, and other signs of systemic involvement.

  • Blood Tests: Blood tests to identify specific antibodies associated with autoimmune diseases, such as antinuclear antibodies (ANA) and scleroderma-specific antibodies.

  • Imaging Studies: Chest X-rays, CT scans, and echocardiograms may be used to evaluate lung and heart involvement.

  • Pulmonary Function Tests: To assess lung function and determine the extent of respiratory involvement.

  • Skin Biopsy: In some cases, a skin biopsy may be performed to confirm the diagnosis by examining tissue under a microscope.

     

Treatment at Felix Hospital

At Felix Hospital, we take a multidisciplinary approach to treating progressive systemic sclerosis, combining the expertise of rheumatologists, pulmonologists, cardiologists, and other specialists to provide comprehensive care.

1. Medication Management: The primary aim of medication in treating SPS is to manage symptoms, slow disease progression, and prevent organ damage. Commonly used medications include:

  • Immunosuppressants: Drugs like methotrexate, mycophenolate mofetil, and cyclophosphamide are used to suppress the immune system and reduce inflammation.

  • Calcium Channel Blockers: For managing Raynaud’s phenomenon and improving blood flow to the fingers and toes.

  • Proton Pump Inhibitors: To treat acid reflux and gastrointestinal symptoms.

  • Anti-inflammatory Drugs: To reduce joint pain and swelling.


2. Physical Therapy: Customized physical therapy programs help maintain mobility and joint function. Our team of physiotherapists works closely with patients to develop exercise plans that improve flexibility and muscle strength.


3. Pulmonary Rehabilitation: For patients with lung involvement, pulmonary rehabilitation programs are designed to improve lung capacity, reduce shortness of breath, and enhance overall quality of life.


4. Dietary and Lifestyle Counseling: Nutritional support is crucial for patients dealing with gastrointestinal complications. Our dietitians provide tailored dietary plans that focus on maintaining digestive health and overall well-being.


5. Advanced Therapeutic Options: For severe cases, advanced treatments of progressive systemic sclerosis such as biologic therapies or stem cell transplantation may be recommended. Felix Hospital stays at the forefront of medical advancements, offering the latest treatments to our patients.


6. Regular Monitoring: progressive systemic sclerosis is a chronic disease that requires ongoing monitoring. At Felix Hospital, we schedule regular follow-up visits to track the progression of the disease, adjust treatment plans, and address any new symptoms or complications.

 

Why Choose Felix Hospital?

Felix Hospital is committed to delivering world-class care for patients with progressive systemic sclerosis. Our multidisciplinary team of experts, led by Dr. Kiran Seth, ensures that each patient receives personalized, comprehensive care tailored to their specific needs. Dr. Kiran Seth's expertise in autoimmune diseases and systemic conditions plays a pivotal role in providing accurate diagnosis and effective treatment strategies of progressive systemic sclerosis, ensuring the best possible outcomes for our patients.

State-of-the-Art Facilities: We offer cutting-edge diagnostic tools and treatment options to ensure the best possible outcomes.

Experienced Specialists: Our team includes highly trained rheumatologists, pulmonologists, cardiologists, and other specialists with expertise in managing autoimmune diseases like SPS.

Holistic Approach: We focus on both the physical and emotional well-being of our patients, offering support throughout the treatment journey.


For expert care and personalized treatment of progressive systemic sclerosis, contact Felix Hospital today. Call us at +91 9667064100 to schedule an appointment.
 

FAQs

1. What causes progressive systemic sclerosis?

  progressive systemic sclerosis is an autoimmune disorder where the immune system attacks the body’s tissues, leading to the overproduction of collagen. The exact cause remains unknown, but genetic and environmental factors may play a role.


2. Can SPS be cured?

  Currently, there is no cure for SPS, but early diagnosis and effective management can slow the progression of the disease and improve quality of life.


3. How is progressive systemic sclerosis different from localized scleroderma?

  progressive systemic sclerosis affects multiple organs and systems, while localized scleroderma mainly affects the skin and tissues beneath it without involving internal organs.


4. What are the risk factors for developing SPS?

  Risk factors include a family history of autoimmune diseases, exposure to certain environmental triggers, and being female, as women are more likely to develop SPS than men.


5. What should I expect during my first visit to Felix Hospital for SPS?

  During your first visit, you will undergo a thorough evaluation that includes a physical examination, medical history review, and necessary diagnostic tests to assess the severity of your condition.


6. Can lifestyle changes help manage SPS?

  Yes, lifestyle modifications such as regular physical activity, a healthy diet, and avoiding cold exposure can help manage symptoms and improve overall well-being.


7. How do I schedule an appointment at Felix Hospital?

  You can easily schedule an appointment by calling our helpline at +91 9667064100 or visiting our website to book a consultation online.

 

At Felix Hospital, we are committed to providing compassionate, top-quality care for patients with progressive systemic sclerosis. Let us help you manage your condition and improve your quality of life. Reach out to us today!